A rare sinonasal tumour with orbital manifestation: glomangiopericytoma

Authors

  • Hui Jean Yap Department of Otorhinolaryngology, Hospital Sultanah Bahiyah, Kedah
  • Ida Sadja'ah Sachlin Department of Otorhinolaryngology, Hospital Sultanah Bahiyah, Kedah
  • Bee Lian Khaw Department of Otorhinolaryngology, Hospital Sultanah Bahiyah, Kedah

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20175636

Keywords:

Glomangiopericytoma, Sinonasal tumour

Abstract

Sinonasal glomangiopericytoma is a tumor showing similarities to a glomus tumour but is less aggressive and has a lower malignancy potential. It was initially reported by Stout and Murray in 1942. Our patient was a 19 years old lady who presented to us with unilateral epistaxis during her pregnancy. Further investigations including a nasopharyngeal biopsy showed signs of an aggressive behaving sinonasal glomangiopericytoma. She underwent left medial maxillectomy via lateral rhinotomy approach to achieve complete excision of the tumor. This was vital as past literatures suggest that incomplete excision of tumor is the most pertinent factor to tumor recurrence. Distant metastasis is rare. Complete excision with regular long term follow up is the treatment of choice. The role of chemo and radiotherapy remains controversial. 

Author Biographies

Hui Jean Yap, Department of Otorhinolaryngology, Hospital Sultanah Bahiyah, Kedah

Department of Otorhinolaryngology

Ida Sadja'ah Sachlin, Department of Otorhinolaryngology, Hospital Sultanah Bahiyah, Kedah

Department of Otorhinolaryngology

Bee Lian Khaw, Department of Otorhinolaryngology, Hospital Sultanah Bahiyah, Kedah

Department of Otorhinolaryngology

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Published

2017-12-22