Nasal neuroglial heterotropia: a rare mimicker of dermoid cyst: a case report

Jayapriya D.; Vikram Raj Mohanam T. C.; Mary Kurien; Kalaiarasan S.; Ninan Zachariah; Raghul T.; Arthy R. G.

doi:10.18203/issn.2454-5929.ijohns20253001

Authors

Jayapriya D. Department of Otorhinolaryngology, AVMC, Kirumampakkam, Pondicherry, India
Vikram Raj Mohanam T. C. Department of Otorhinolaryngology, AVMC, Kirumampakkam, Pondicherry, India
Mary Kurien Department of ENT, Pondicherry Institute of Medical Sciences, Puducherry, India
Kalaiarasan S. Department of Pathology, AVMC, Kirumampakkam, Pondicherry, India
Ninan Zachariah Department of Pediatrics Surgery, Pondicherry Institute of Medical Sciences, Puducherry, India
Raghul T. Department of ENT, AMC multi-specialty hospital Tirupur, Tamil Nadu, India
Arthy R. G. Department of ENT, Pondicherry Institute of Medical Sciences, Puducherry, India

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20253001

Keywords:

Frontonasal mass, Midline nasal mass, Nasal glial heterotopia, Nasal glioma

Abstract

We report an uncommon case of nasal neuroglial heterotopia (NGH, glioma) presenting as midline nasal mass. Review of literature, imaging challenged and surgical management options are discussed. Unlike the more common nasal dermoid, 20% of NGH have intracranial communication which can cause post-operative life-threatening complications like CSF leak and meningitis.

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