Congenital arhinia: a highly unexpected presentation

Authors

  • Anju Elizabeth Mathai Department of ENT, Sur hospital, Ministry of health, Sultanate of Oman
  • Pushpendra Shekhawat Department of ENT, Sur hospital, Ministry of health, Sultanate of Oman
  • Nasser Al Tamami Department of ENT, Sultan Qaboos University Hospital, Sultanate of Oman
  • Dimple Shekhawat Kasturba Medical College, Manipal, India https://orcid.org/0009-0002-6667-8589

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20250347

Keywords:

Arrhinia, Multidisciplinary approach, Facial anomalies

Abstract

Congenital nasal absence (arhinia) is an extremely rare malformation. Arhinia causes severe airway obstruction and poor feeding in the affected neonate. There is an association with other facial anomalies, especially defects of the eyes, ears, palate, and midline defects. In this article, we present a 16-month-old child born with absent nose, microphthalmia and cleft palate. Such patients require multidisciplinary team approach for appropriate care and management.

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References

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Published

2025-02-06

How to Cite

Elizabeth Mathai, A., Shekhawat, P., Tamami, N. A., & Shekhawat, D. (2025). Congenital arhinia: a highly unexpected presentation. International Journal of Otorhinolaryngology and Head and Neck Surgery, 11(2), 150–152. https://doi.org/10.18203/issn.2454-5929.ijohns20250347

Issue

Section

Case Reports