A rare case of temporal bone chondrosarcoma
DOI:
https://doi.org/10.18203/issn.2454-5929.ijohns20231821Keywords:
Chondrosarcoma, Petrous apex lesion, Temporal bone chondrosarcoma, Osseo-cartilagenous tumour of skullAbstract
A rare case of lateral skullbase lesion, in a 24-year female, presented with moderately severe conductive type hearing loss, and facial paralysis. Audiological and radiological investigations were done which could not provide a reasonably certain diagnosis. So the patient was taken up for surgery. A subtotal pertrosectomy with blind sac closure was done. The histopathological analysis showed the lesion to be moderately differentiated chondrosracoma, an osseocartilagenous malignancy of the temporal bone. Due to rare nature, difficult location near vital structures, local invasiveness and potential for complications, diagnosis and treatment is difficult.
References
Cianfriglia F, Pompili A, Occhipinti E. Intracranial malignant cartilaginous tumours. Report of two cases and review of literature. Acta Neurochir (Wien). 1978;45:163-75.
Thorkildsen J, Taksdal I, Bjerkehagen B, Haugland HK, Børge Johannesen T, Viset T, et al. Chondrosarcoma in Norway 1990-2013; an epidemiological and prognostic observational study of a complete national cohort. Acta Oncol. 2019;58(3):273-82.
Cendekiawan T, Wong R, Rabie A. Relationships between cranialbase synchondroses and craniofacial development: a review. Open Anat J. 2010;2:67-75.
Raghu M, Moumoulidis I, De R, Moffat D. Chondrosarcomas of the temporal bone: presentation and management. J Laryngol Otol. 2004;118(7):551-5.
House JW, Brackmann DE. Facial nerve grading system. Otolaryngol Head Neck Surg. 1985;93(2):146-7.
Baehring J M, Piepmeier J, Duncan C, Ogle E, Kim J, Liebsch N. Chondrosarcoma of the skull base. J Neurooncol. 2006;76:49.