DOI: https://dx.doi.org/10.18203/issn.2454-5929.ijohns20221652
Published: 2022-06-24

Fibrous dysplasia of the paranasal sinuses: case report

Sara Halily, Youssef Oukessou, Sara Moujrid, Sami Rouadi, Reda Abada, Mohamed Roubal, Mohamed Mahtar

Abstract


Fibrous dysplasia (FD) is a rare congenital non-malignant bone tumor that affects the skeletal system development and interferes with normal bone formation. It’s non-hereditary and its exact cause remains unknown. The condition is characterized by fibro-osseous connective tissue gradually replacing normal bone and marrow leading to the formation of bone that’s fragile and prone to fractures. It is not uncommon for the disease to affect craniofacial bones but the sinonasal cavity involvement remains extremely rare. We presented a case of an 80-years-old male patient who reported nasal obstruction and a long-term swelling in the upper jaw that dates back over 20 years resulting in facial deformities and unilateral proptosis from compression exerted on the eye by the tumor. The patient reported having taken drugs to treat symptoms especially nasal congestion. But his dyspnea persisted. Physical examination, computed tomography (CT) scan and MRI have been elaborated and discussed. And on last resort, surgery was recommended.


Keywords


Fibrous dysplasia, Paranasal sinuses, Optic nerve, Facial deformity

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