Published: 2021-03-24

Juvenile ossifying fibroma of the orbit: a rare location

Pedro Clarós, Sofia Polainas, Marta Fortuny, Andres Clarós


Osseous tumors in the craniofacial skeleton of young patients are not very frequent, and tumors involving the walls of the orbital cavity are even more infrequent. Despite being usually slow-growing, even small neoformations can have a local aggressive behavior, displacing and compressing vital structures, and so it is important to perform an early diagnosis in order to avoid the tumor to pose problems on the optic nerve and threaten vision. The case that we are presenting shows an ossifying fibroma in a 19-year-old male from Ethiopia, a benign lesion whose progressive growth caused proptosis and downward displacement of the left eye. Following an adequate radiological diagnosis, we were able to delimit the fibroma existence and location. The surgery was conducted in a conservative form, allowing the patient not to suffer from post-surgery malformations. Histopathological diagnosis was compatible with juvenile ossifying fibroma, psammomatoid variant, arising from an uncommon location – the roof of the orbit.  


Ossifying fibroma, Orbital tumor, Benign tumor

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Nicolai P, Castelnuovo P. Benign Tumors of the Sinonasal Tract. In: Paul W. Flint PW, Haugh BH, Lund V, Niparko JK, K. Thomas Robbins, Thomas JR, Lesperance MM, editors. Cumm Otolaryngol Head Neck Surg. 2015:740-51.

Lemoine S, Cassagnau E, Bertin H, Poisson M, Corre P, Guiol J. Juvenile ossifying fibroma: case report and literature review. Management and differential diagnosis. J Oral Med Oral Surg 2018;24:67-71.

Linhares P, Pires E, Carvalho B, Vaz R. Juvenile psammomatoid ossifying fibroma of the orbit and paranasal sinuses. A case report. Acta Neurochir 2011;153:1983-8.

Maiorano E, Slootweg PJ. Maxillofacial Skeleton and Teeth. In: Cardesa A, Slootweg PJ, Gale N, Franchi A, editors. Pathology of the Head and Neck. 2nd ed. Springer. 2016:179-227.

Chrcanovic BR, Gomez RS. Juvenile ossifying fibroma of the jaws and paranasal sinuses: a systematic review of the cases reported in the literature. Int J Oral Maxillofac Surg 2020;49:28-37.

Cruz A, Alencar V, Figueiredo A, De Paula S, Eichenberger G, Chahud F, et al. Ossifying Fibroma: A rare cause of orbital inflammation. Ophthal Plast Reconstr Surg. 2008;24:107–12.

Wakefield MJ, Ross AH, Damato EM, Salvi SM, Baker GRC. Review of Lateral Orbital wall Ossifying Fibroma. Orbit 2010;29(6):317-20.

Lyons CJ. Other mesenchymal abnormalities. In: Lambert S, Lyons C. Taylor and Hoyt's Pediatric Ophthalmology and Strabismus. Elsevier Inc. 2017:2328