Cochlear implantation in osteogenesis imperfecta in India: a case report

Authors

  • Rajesh Kumar Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.
  • Ashvanee Kumar Chaudhary Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.
  • Sunil Kumar Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.
  • Vishwambhar Singh Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.
  • Ashutosh A. Abinashi Department of Otorhinolaryngology, Government Medical College, Azamgarh, U.P.
  • Subhadeep Das Department of Otorhinolaryngology, North Eastern Indira Gandhi Regional Institute of Health and Medical Sciences, Shillong, Meghalaya

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20210179

Keywords:

Cochlear implant, Osteogenesis imperfecta, Facial twitching, COLIA-1 and COLIA-2, Type-1 collagen, Rheumatic heart disease

Abstract

A 25 years old male patient with osteogenesis imperfecta presented with bilateral profound hearing loss, not benefitted with hearing aid. Cochlear implantation of 12 channel intracochlear implant was done successfully, intracochlear insertion of the 12 electrodes resulted in hearing improvement of 80 dB at frequency 250 Hz to 4 KHz. The patient complained of facial twitching on first visit after switching on speech processer device, reducing the current level at the electrode 6 abolished the non-acoustic nerve excitation with preservation of acoustic performances. Osteogenesis imperfecta patient may involve a risk for non-acoustic nerve activation in cochlear implant patients possibly resulting from a decrease impedance to current spread, it happens because of abnormal bone tissue. Non acoustic nerve activation can be overcome by modification in mapping.

Author Biographies

Rajesh Kumar, Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.

Professor ,  Department of Otorhinolaryngology

Ashvanee Kumar Chaudhary, Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.

Senior Resident,Otorhinolaryngology

Sunil Kumar, Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.

Audiologist , Department  of Otorhinolaryngology

Vishwambhar Singh, Department of Otorhinolaryngology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, U.P.

Associate Professor, Department of Otorhinolaryngology,

Ashutosh A. Abinashi, Department of Otorhinolaryngology, Government Medical College, Azamgarh, U.P.

Senior Resident , Department of Otorhinolaryngology

Subhadeep Das, Department of Otorhinolaryngology, North Eastern Indira Gandhi Regional Institute of Health and Medical Sciences, Shillong, Meghalaya

Senior Resident, Department of Otorhinolaryngology

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Published

2021-01-25

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Section

Case Reports