Recurrent dermatofibrosarcoma protuberans of head and neck with fibrosarcomatous change: a challenge for the head and neck surgeon


  • Balaji Ramamourthy Department of Otolaryngology, Head and Neck Surgery, PGIMER, Chandigarh, India
  • Kanika Arora Department of Otolaryngology, Head and Neck Surgery, PGIMER, Chandigarh, India
  • Balamurugan Thirunavukkarasu Department of Histopathology, PGIMER, Chandigarh, India
  • Anurag S. Ramavat Department of Otolaryngology, Head and Neck Surgery, PGIMER, Chandigarh, India
  • Amanjit Bal Department of Otolaryngology, Head and Neck Surgery, PGIMER, Chandigarh, India



Dermatofibrosarcoma protuberans, Head and neck, Recurrent, Fibrosarcoma


Dermatofibrosarcoma protuberans (DFSP) of head and neck is a rare, slow growing, intermediate to low grade malignant soft tissue neoplasm with high rates of local recurrence requiring multiple surgeries posing great distress for both the patient and treating physician alike. Fibrasarcomatous change is a very rare occurrence in such tumors increasing risk of distant metastasis. We report such a rare case of recurrent DFSP with fibrosarcomatous change of the head and neck region, the management protocol and the key points a surgeon should keep in mind while treating such patients.



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