DOI: http://dx.doi.org/10.18203/issn.2454-5929.ijohns20200636

Ewing’s sarcoma of sinonasal tract: a rare case

Ankur Gupta, Ancy S. Sofia, Kanwar Sen

Abstract


Extra skeletal Ewing’s sarcoma (EES) is a rare, rapidly growing, round cell malignant tumour that can develop in the soft tissue at any location. Involvement of the paranasal sinus is a very rare entity. Nearly 80% of patients are younger than 20 years. Diagnosis is made after histopathological examination, immunohistochemical studies and cytogenetic studies. Treatment includes a multidisciplinary approach with surgery as the first line followed by chemotherapy and radiotherapy.

 


Keywords


Ewing’s sarcoma, EES, Peripheral neuroectodermal tumor, Paranasal sinus

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References


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