Ewing’s sarcoma of sinonasal tract: a rare case

Authors

  • Ankur Gupta Department of ENT, PGIMER Dr RML Hospital, New Delhi
  • Ancy S. Sofia Department of ENT, PGIMER Dr RML Hospital, New Delhi
  • Kanwar Sen Department of ENT, PGIMER Dr RML Hospital, New Delhi

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20200636

Keywords:

Ewing’s sarcoma, EES, Peripheral neuroectodermal tumor, Paranasal sinus

Abstract

Extra skeletal Ewing’s sarcoma (EES) is a rare, rapidly growing, round cell malignant tumour that can develop in the soft tissue at any location. Involvement of the paranasal sinus is a very rare entity. Nearly 80% of patients are younger than 20 years. Diagnosis is made after histopathological examination, immunohistochemical studies and cytogenetic studies. Treatment includes a multidisciplinary approach with surgery as the first line followed by chemotherapy and radiotherapy.

 

Author Biographies

Ankur Gupta, Department of ENT, PGIMER Dr RML Hospital, New Delhi

ENT department

Specialist

Ancy S. Sofia, Department of ENT, PGIMER Dr RML Hospital, New Delhi

ENT department Dr RML hospital

Post graduate

Kanwar Sen, Department of ENT, PGIMER Dr RML Hospital, New Delhi

ENT department

Head of department

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Published

2020-02-24

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Section

Case Reports