Nasal polyposis with dextrocardia, pulmonary agenesis and microtia: Goldenhar syndrome - a case report

Authors

  • Preeti Dhingra Department of ENT and Head Neck Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra, India
  • Christopher de Souza Department of ENT and Head Neck Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra, India
  • Kamal Parsram Department of ENT and Head Neck Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20200640

Keywords:

Goldenhar syndrome, Dextrocardia, Pulmonary agenesis

Abstract

Its a case report of, Goldenhar syndrome (GS), a rare syndrome with right ear microtia, atresia of the external auditory canal, nasal polyposis, pulmonary agenesis, spine abnormalities and dextrocardia. This case, has showed the involvement of nose in the form of nasal polyposis in GS, which has never been reported in the literature so far.

Author Biography

Preeti Dhingra, Department of ENT and Head Neck Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra, India

junior consultant

ENT Head and neck surgery

lilavati hospital

References

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Published

2020-02-24

Issue

Section

Case Reports