Rhabdomyoma of the tongue base

Authors

  • Julius M. Vahl Department of ENT, University Hospital Ulm, Ulm, http://orcid.org/0000-0002-4481-7085
  • Lisa Baumann Department of Pathology, University Hospital Ulm, Ulm
  • Thomas K. Hoffmann Department of ENT, University Hospital Ulm, Ulm,

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20194955

Keywords:

Mesenchymal tumor, Soft tissue tumor, Head and neck, Tuberous sclerosis, Tumoral laser surgery

Abstract

Extracardiac rhabdomyoma is a very rare condition with potentially multifocal manifestations including the head and neck region. We present a case of an 81-year-old patient who presented as a medical emergency because of ambiguous, progressive throat pain and dysphagia. After diagnostic work up including magnetic resonance (MR) scan and biopsy a rhabdomyoma of the tongue base was diagnosed. The tumor was completely excised by transoral laser microsurgery and the patient’s symptoms vanished. This case report is described in context of the current literature with a discussion of diagnostic steps and treatment options of rhabdomyoma in the head and neck region. Rhabdomyoma is a rare, but nevertheless relevant differential diagnosis of head and neck tumors.

Author Biographies

Julius M. Vahl, Department of ENT, University Hospital Ulm, Ulm,

Otorhinolaryngology

Thomas K. Hoffmann, Department of ENT, University Hospital Ulm, Ulm,

Otorhinolaryngology

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Published

2019-10-23