Kimura disease of the supraauricular region: a rare presentation


  • Firamir Bin Zulkifli Department of Otorhinolaryngology- Head and Neck Surgery, Hospital Queen Elizabeth, Kota Kinabalu, Sabah, Kuala Lumpur, Malaysia
  • Mawaddah Binti Azman Department of Otorhinolaryngology- Head and Neck Surgery, University of Kebangsaan Malaysia Medical Centre, Kuala Lumpur, Malaysia
  • Loong Siow Ping Department of Otorhinolaryngology- Head and Neck Surgery, Hospital Queen Elizabeth, Kota Kinabalu, Sabah, Kuala Lumpur, Malaysia



Kimura’s disease, Head and neck, Supra-auricular


Kimura disease is an idiopathic chronic inflammatory disorder involving the subcutaneous tissue. It favors the head and neck region, although presentation over atypical sites has been reported. This disease occurs spontaneously, has a characteristic indolent growth pattern but has a high tendency to recur locally after treatment. Due to its benign nature, there is still no clear consensus on the optimal management of this rare disorder. Various treatment options are available which include systemic steroids, antihistamines, immunosuppressant, chemotherapy, radiotherapy, and surgical excision. Presently, the disease remains a therapeutic enigma as the pathogenesis is still a mystery and its tendency to recur following treatment proves to be discouraging. Herein we report a rare case of Kimura disease involving the supra-auricular region who underwent surgical excision.


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