Castleman’s disease presenting as parotid mass: a case report


  • Ankur Batra Department of Otorhinolaryngology and Head & Neck Surgery, Yatharth Superspeciality Hospital, Noida, India
  • Megha Goyal Department of Otorhinolaryngology and Head & Neck Surgery, ESIC Hospital, Sahibabad, Ghaziabad, Uttar Pradesh, India



Castleman’s disease, Parotid, Head and neck, Salivary gland


Castleman’s disease is a rare, benign, lymphoproliferative disorder of unknown etiology. It can involve any lymph node group in the body with mediastinum being the commonest site. Salivary glands are affected rarely. We report a 35 year old male patient who presented with slowly progressive, painless right sided parotid swelling for 3 years. Clinical examination showed a 4×3 cm single, firm, non-tender, non-pulsatile swelling with smooth surface and normal overlying skin present in the right parotid region. Magnetic resonance imaging (MRI) revealed a well-defined hyper-intense mass lesion on T2 measuring 3.9×3×2.8 cm and Fine needle aspiration cytology (FNAC) showed intense lymphoplasmacytic infiltrates. No conclusive diagnosis could be made on the basis of FNAC. So, the excision of parotid mass with facial nerve preservation was done. The final histopathology confirmed the diagnosis as Castleman’s disease. Although Castleman’s disease in the parotid gland is rare, clinicians should consider it as the differential diagnosis of any solid tumors that exhibit non-specific presenting characteristics and surgical excision is preferred treatment for unicentric disease.


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Case Reports